Néoplasies myéloprolifératives (NMP) – Partie 2 : Guide infirmier sur la conduite à tenir devant les symptômes de NMP

Sabrina Fowlkes, Cindy Murray, Adrienne Fulford, Tammy De Gelder, Nancy Siddiq

Abstract


Les néoplasies myéloprolifératives (NMP) sont des troubles rares mais potentiellement mortels causés par la production excessive de cellules souches dans la moelle osseuse. Chez les patients atteints de NMP sans mutation du gène BCR-ABL1 (c.-à-d. la thrombocytémie essentielle [TE], la polycythémie vraie [PV] et la myélofibrose [MF], aussi appelées « NMP classiques »), les symptômes peuvent être incapacitants et nuire à la qualité de vie. Malgré tout, il est possible pour les patients souffrant de ces types de NMP de vivre plusieurs années, moyennant un traitement et un suivi à long terme. Les infirmières jouent alors un rôle essentiel pour favoriser la communication avec ces patients, évaluer les symptômes et leur enseigner les traitements et les stratégies d’autosoins pouvant les apaiser. Le présent article, second d’une série de deux, présentera aux infirmières et autres professionnels de la santé des conseils pratiques pour traiter la symptomatologie associée aux NMP et ainsi améliorer la santé générale et la qualité de vie des patients.


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References


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